alpha L Iduronidase

《英文msh詞典》alpha L Iduronidase
[入口詞] alpha L Iduronidase
[主題詞] Iduronidase
[英文釋義] An enzyme that hydrolyzes iduronosidic linkages in desulfated dermatan. Deficiency of this enzyme produces Hurler's syndrome. EC 3.2.1.76.